Cor Vasa 2022, 64(6):657-660 | DOI: 10.33678/cor.2022.016

Surgical Appearance of Aortic Involvement in Erdheim-Chester Disease: A Report of Two Cases

Umit Arslana, Ferhat Borulua, Oktay Tüydeşb, Sevilay Ozmenc, Bilgehan Erkut
a Department of Cardiovascular Surgery, Faculty of Medicine, Ataturk University, Erzurum, Turkey
b Department of Cardiovascular Surgery, Bingöl State Hospital, Bingöl, Turkey
c Department of Medical Pathology Faculty of Medicine, Ataturk University, Erzurum, Turkey

Erdheim-Chester disease (ECD), known as histiocytic neoplastic disease, can be diagnosed as a peripheral arterial disease because of its effects on vascular structures. Aortic involvement in ECD is usually recognised radiologically. However, there is insufficient information about the surgical appearance and treatment of aortic involvement in ECD. In this report, we presented a patient with ascending aortic involvement detected incidentally during coronary bypass and a patient with abdominal aortic involvement mimicking aortoiliac disease.

Keywords: Abdominal aorta, Ascending aorta, Coated aorta, Erdheim-Chester disease

Received: February 7, 2022; Revised: February 27, 2022; Accepted: March 2, 2022; Published: December 15, 2022  Show citation

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Arslan U, Borulu F, Tüydeş O, Ozmen S, Erkut B. Surgical Appearance of Aortic Involvement in Erdheim-Chester Disease: A Report of Two Cases. Cor Vasa. 2022;64(6):657-660. doi: 10.33678/cor.2022.016.
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