Cor Vasa 2024, 66(5):529-533 | DOI: 10.33678/cor.2024.066

(Complex treatment and its complications in a patient with hypertrophic cardiomyopathy)

Zuzana Holubcová^a, Matej Strýček^a, Rostislav Polášek^{a, b}, Pavol Tomašov^{a, b}

^a Kardiocentrum, Krajská nemocnice Liberec, Liberec, Česká republika

^b Fakulta zdravotnických studií, Technická univerzita v Liberci, Liberec, Česká republika

Hypertrophic cardiomyopathy is a genetic disorder characterized by increased left ventricle thickness greater than 15 milimetres in the absence of any other explanatory cause. The diagnostics and treatment of patients with hypertrophic cardiomyopathy include search for a management of left ventricular outflow tract obstruction, risk stratification for sudden cardiac death and genetic testing and screening of family members. This case report describes a young man with a chronic skin disease on permanent biological therapy who had a family history of sudden cardiac death and had recently been diagnosed with hypertrophic cardiomyopathy with symptomatic left ventricular outflow tract obstruction. An alcohol septal ablation had been indicated, resulting in improved hemodynamic and clinical outcome. An implantable cardioverter-defibrillator was implanted for the primary prevention of sudden cardiac death. However, an early device pocket infection due to the patient's skin disease and the development of reactive pericarditis led to complications.

Keywords: Hypertrophic cardiomyopathy, Septal reduction therapy, Sudden death

Received: April 15, 2024; Revised: April 15, 2024; Accepted: August 26, 2024; Prepublished online: June 2, 2012; Published: October 25, 2024  Show citation