Cor Vasa 2022, 64(5):530-532 | DOI: 10.33678/cor.2021.115

Low Oxygen Saturation Following Total Correction in a Patient with Tetralogy of Fallot and Persistant Left Superior Caval Vein - How Did We Diagnose and Manage?

Mehmet Turan Basunlu^a, Senay Coban^a, Gizem Sari^a, Turkay Saritas^a, Abdullah Erdem^a, Didem Melis Oztas^b, Metin Onur Beyaz^c, Emre Oteyaka^d, Yilmaz Yozgat^a, Murat Ugurlucan^d, Halil Turkoglu^d

^a Department of Pediatric Cardiology, Faculty of Medicine, Istanbul Medipol University, Istanbul, Turkey

^b Cardiovascular Surgery Clinic, Istanbul Education and Research Hospital, Istanbul, Turkey

^c Department of Cardiovascular Surgery, Faculty of Medicine, Mustafa Kemal University, Hatay, Turkey

^d Department of Cardiovascular Surgery, Faculty of Medicine, Istanbul Medipol University, Istanbul, Turkey

Association of tetralogy of Fallot (TOF) with the other intracardiac pathologies such as atrial septal defect (ASD), atrioventricular canal defect or persistent left superior vena cava (PLSVC), absent pulmonary valve are well known pathologies. The associated pathologies require specific attention during surgical treatment. In this manuscript, we present management of a four-month-old girl who was diagnosed with TOF and PLSVC but the diagnosis of unroofed coronary sinus was missed in her. Association of unroofed coronary sinus with TOF is a very rare variant of TOF pathology.

Keywords: Atrial septal defect, Coronary sinus type atrial septal defect, Tetralogy of Fallot

Received: September 8, 2021; Revised: September 29, 2021; Accepted: October 3, 2021; Published: November 1, 2022  Show citation