Cor Vasa 2021, 63(5):583-587 | DOI: 10.33678/cor.2021.047

Complete atrio-ventricular canal in natural history. A case in adulthood and a mini-review

Vito Maurizio Paratoa, Camilla Notaristefania, Germana Gizzia, Michele Scaranoa, Alessandra Baldinellib, Marco Pozzib
a Cardiology and Cardiac Rehabilitation Unit, ASUR Marche, Madonna del Soccorso Hospital, San Benedetto del Tronto, Italy
b Pediatric Cardiology and Cardiac Surgery Unit, GUCH Center, "G.M. Lancisi" University Hospital, Ancona, Italy

The natural history of complete atrio-ventricular septal defect (AVSD) without surgery has been well documented and many authors have reported that only 4% of patients survives beyond 5 years old. Without surgery, most of the deaths in infancy are from severe congestive heart failure caused by the large left-to-right shunt and atrio-ventricular valve incompetence. Deaths after 5 years of age are probably from pulmonary vascular disease that leads to an irreversible pulmonary hypertension burdened by a poor long-term prognosis. We present a case of complete AVSD with a survival till fifth decade of life in whom the defect was associated with a dextrocardia and a common atrium.

Keywords: Adulthood, Complete atrio-ventricular septal defect, Echocardiography, Natural history

Received: March 28, 2021; Revised: March 28, 2021; Accepted: April 5, 2021; Published: October 20, 2021  Show citation

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Parato VM, Notaristefani C, Gizzi G, Scarano M, Baldinelli A, Pozzi M. Complete atrio-ventricular canal in natural history. A case in adulthood and a mini-review. Cor Vasa. 2021;63(5):583-587. doi: 10.33678/cor.2021.047.
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