Cor Vasa 2020, 62(5):483-485 | DOI: 10.33678/cor.2020.076

Long QT Syndrome and Electrical Storm: Is Implanted Cardiac Defibrillator the Final Destination in Long QT Syndrome Management?

Ali A. Al-Mossawi^a, Kasim A. Ismail^a, Zainab A. Dakhil^b

^a Cardiology Department, Ibn Al-Bitar Cardiac Center, Baghdad, Iraq

^b Al-Kindy College of Medicine, Baghdad University, Baghdad, Iraq

Electrical storm is a life-threatening medical emergency and in the context of implantable cardiac defibrillators it is defined as three or more appropriate detections of ventricular arrhythmia in prior 24 hours leading to implantable cardiac defibrillator shocks. Sympathetic stimulation is the forefront player for initiation and maintenance of ventricular arrhythmia. We are reporting a case from an emerging country who has long QT syndrome with implanted cardiac defibrillator and presented with electrical storm, this case highlights the challenges that we face in daily practice during managing this population.

Keywords: Arrhythmogenic syndromes, Emerging country, ICD storm, Psychosocial support, Sympathectomy, Young

Received: May 22, 2020; Revised: July 31, 2020; Accepted: August 2, 2020; Published: November 1, 2020  Show citation